Terkko Navigator / Journal of Cystic Fibrosis

Amplifiers co-translationally enhance CFTR biosynthesis via PCBP1-mediated regulation of CFTR mRNA

In vivo demonstration of Pseudomonas aeruginosa biofilms as independent pharmacological microcompartments

At the forefront of cystic fibrosis Basic Science research: 16th ECFS Basic Science Conference

R117H-CFTR function and response to VX-770 correlate with mRNA and protein expression in intestinal organoids

Lymphocyte responses to Mycobacterium tuberculosis and Mycobacterium bovis are similar between BCG-vaccinated patients with cystic fibrosis and healthy controls

Predictive effects of low birth weight and small for gestational age status on respiratory and nutritional outcomes in cystic fibrosis

Airway profile of bioactive lipids predicts early progression of lung disease in cystic fibrosis

Pseudomonas aeruginosa antibody response in cystic fibrosis decreases rapidly following lung transplantation

Minimal change in structural, functional and inflammatory markers of lung disease in newborn screened infants with cystic fibrosis at one year

Variable cellular ivacaftor concentrations in people with cystic fibrosis on modulator therapy

Unmasking catamenial hemoptysis in the era of CFTR modulator therapy

Efficacy and safety of ataluren in patients with nonsense-mutation cystic fibrosis not receiving chronic inhaled aminoglycosides: The international, randomized, double-blind, placebo-controlled Ataluren Confirmatory Trial in Cystic Fibrosis (ACT CF)

Identification of Mycobacterium porcinum in patients with cystic Fibrosis: Pathogen or contaminant?

Glycemic control and FEV1 recovery during pulmonary exacerbations in pediatric cystic fibrosis-related diabetes

Abnormal glucose tolerance and the 50-gram glucose challenge test in Cystic fibrosis

Organizing pneumonia secondary to Exophiala dermatitidis in cystic fibrosis: A case report

New approaches to genetic therapies for cystic fibrosis

Sputum trypsin-like protease activity relates to clinical outcome in cystic fibrosis

Exploring the basic mechanisms in Cystic Fibrosis: Promoting data presentation and discussion at the 16th ECFS Basic Science Conference

Evaluation of the exercise intensity generated by active video gaming in patients with cystic fibrosis and healthy individuals

Clinical effect of lumacaftor/ivacaftor in F508del homozygous CF patients with FEV1 ≥ 90% predicted at baseline

Developing a smartphone application to support social connectedness and wellbeing in young people with cystic fibrosis

Towards next generation therapies for cystic fibrosis: Folding, function and pharmacology of CFTR

Adherence to lumacaftor-ivacaftor therapy in patients with cystic fibrosis in France

The influence of CFTR complex alleles on precision therapy of cystic fibrosis

News Article

To be or not to be on CFTR modulators during pregnancy: Risks to be considered

The genetics and genomics of cystic fibrosis

Utilizing centralized biorepository samples for biomarkers of cystic fibrosis lung disease severity

Rapid lung function decline in adults with early-stage cystic fibrosis lung disease

Structured surveillance of Achromobacter, Pandoraea and Ralstonia species from patients in England with cystic fibrosis

Prevalence of unmet palliative care needs in adults with cystic fibrosis

Lumacaftor/ivacaftor reduces exacerbations in adults homozygous for Phe508del mutation with severe lung disease

Nutritional excess in cystic fibrosis: the skinny on obesity

Expanding access to CFTR modulators for rare mutations: The utility of n-of-1 trials

Functional rescue of c.3846G>A (W1282X) in patient-derived nasal cultures achieved by inhibition of nonsense mediated decay and protein modulators with complementary mechanisms of action

Strong toll-like receptor responses in cystic fibrosis patients are associated with higher lung function

CFTR-deficient pigs display alterations of bone microarchitecture and composition at birth

Intestinal organoids for Cystic Fibrosis research

Ivacaftor in cystic fibrosis with residual function: Lung function results from an N-of-1 study

Integrating the multiple breath washout test into international multicentre trials

Positive clinical outcomes following ivacaftor treatment in a cystic fibrosis patient with the genotype 3272–26A > G/Q493X

CFTR: New insights into structure and function and implications for modulation by small molecules

Streptococcus pseudopneumoniae, an opportunistic pathogen in patients with cystic fibrosis

Can exercise replace airway clearance techniques in cystic fibrosis? A survey of patients and healthcare professionals

Forskolin-induced swelling of intestinal organoids correlates with disease severity in adults with cystic fibrosis and homozygous F508del mutations

Characterising burden of treatment in cystic fibrosis to identify priority areas for clinical trials

Genetic variation in CFTR and modifier loci may modulate cystic fibrosis disease severity

Prevalence and factors associated with overweight and obesity in adults with cystic fibrosis: A single-center analysis

Regional differences in infection and structural lung disease in infants and young children with cystic fibrosis